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Glycosaminoglycan metabolism
SuperPath
Pathway network
for
Glycosaminoglycan metabolism
SuperPath
22
Pathways
in the
Glycosaminoglycan metabolism
SuperPath
MPS I - Hurler syndrome
Defective HEXA causes GM2G1
MPS II - Hunter syndrome
Glycosaminoglycan degradation
MPS IX - Natowicz syndrome
MPS IIIA - Sanfilippo syndrome A
MPS VII - Sly syndrome
Heparan sulfate/heparin (HS-GAG) metabolism
MPS IIID - Sanfilippo syndrome D
Hyaluronan biosynthesis and export
chondroitin sulfate biosynthesis (late stages)
Metabolism of carbohydrates
Mucopolysaccharidoses
MPS IIIB - Sanfilippo syndrome B
MPS IV - Morquio syndrome A
Glycosaminoglycan metabolism
HS-GAG biosynthesis
Defective HEXB causes GM2G2
MPS VI - Maroteaux-Lamy syndrome
MPS IIIC - Sanfilippo syndrome C
Hyaluronan metabolism
Hyaluronan uptake and degradation
298
Genes
in the
Glycosaminoglycan metabolism
SuperPath
GUSB
HYAL1
IDUA
HEXA
IDS
HGSNAT
HEXB
NAGLU
SGSH
GALNS
GLB1
GNS
ARSB
HYAL2
HPSE
HPSE2
GPC6
SLC35D2
EXT1
EXT2
GPC2
HS3ST5
GPC4
GPC5
GLCE
HS6ST3
GPC3
GPC1
HSPG2
NDST1
AGRN
SDC1
SDC2
SDC4
NDST4
HS3ST6
NDST2
HS6ST2
NDST3
HS6ST1
HS2ST1
SDC3
HS3ST4
HS3ST3B1
HS3ST3A1
HS3ST2
HS3ST1
ABCC5
HAS1
HAS2
HAS3
CEMIP
LYVE1
CHP1
HMMR
STAB2
SLC9A1
HYAL3
CD44
CSPG5
B4GALT7
B3GALT6
B3GAT2
VCAN
NCAN
CSPG4
DCN
B3GAT3
B3GAT1
BGN
BCAN
XYLT1
XYLT2
GLB1L
CHST1
CHST15
CHST3
CHST13
CHST11
CHST12
CHST7
UST
B3GNT3
ST3GAL6
B3GNT2
SLC26A1
B4GAT1
KERA
CHST14
ACAN
SLC26A2
CHSY1
FMOD
CHST5
B4GALT1
DSE
CHSY3
SLC35B2
LUM
CHST6
OMD
OGN
SLC35B3
CHPF2
CSGALNACT2
PRELP
CSGALNACT1
ST3GAL1
ST3GAL2
ST3GAL4
ST3GAL3
B3GNT4
CHPF
CHST9
B4GALT4
B4GALT3
B4GALT2
PAPSS2
PAPSS1
DSEL
B3GNT7
B4GALT6
B4GALT5
CHST2
HYAL4
GNPDA1
SLC25A13
B3GALT5
AKR1A1
FUT9
NUP50
NUP42
B4GALNT2
NUP35
GLYCTK
GNPDA2
SLC25A10
FUT11
AGL
ENO1
ENO2
ENO3
ALDH1A1
SLC37A2
FBP1
PRPS1L1
ALDOA
ALDOB
RPIA
ALDOC
AKR1B1
NUP205
NUP210
NUP160
MAN2B2
NUP188
NUP62
SHPK
FUT1
FUT2
FUT3
FUT4
FUT5
FUT6
FUT7
G6PC1
G6PD
SLC37A4
GAA
PGLS
GALE
GALK1
GALT
GAPDH
TKFC
GBE1
GAPDHS
GCK
GCKR
ABO
GOT1
GOT2
GPI
PGM2L1
PGP
GYG1
GYS1
GYS2
ST6GALNAC6
HK1
HK2
HK3
NUP43
NHLRC1
KHK
ENO4
LALBA
MAN2C1
MAN2B1
MANBA
MDH1
MDH2
NUP88
NUP98
PC
PCK1
PCK2
DERA
CRYL1
DCXR
PFKFB1
PFKFB2
PFKFB3
PFKFB4
PFKL
PFKM
PFKP
PGAM1
PGAM2
PGD
PGK1
PGK2
PGM1
PHKA1
PHKA2
PHKB
PHKG1
PHKG2
PKLR
PKM
NUP54
SLC37A1
PPP1R3C
PPP2CA
PPP2CB
PPP2R1A
PPP2R1B
PGM2
PPP2R5D
PRKACA
PRKACB
PRKACG
NDC1
NUP133
PRPS1
PRPS2
NUP107
G6PC2
PYGB
PYGL
PYGM
RANBP2
RHCE
RHD
RPE
RPS27A
SEC13
RBKS
SLC2A1
SLC25A1
SORD
BPGM
TALDO1
TKT
TPI1
TPR
RPEL1
UBA52
UBB
UBC
UGP2
NUP37
EPM2A
NUP85
CALM1
HKDC1
NUP214
CALM2
CALM3
AAAS
SEH1L
ADPGK
SLC25A11
FUT10
RAE1
SLC25A12
B3GALT4
B3GALT2
B3GALT1
FBP2
GYG2
G6PC3
NUP155
NUP93
NUP58
POM121
XYLB
NUP153
*Darkness represents the genes rank within the SuperPath, via the multiplicity of each gene in the constituent pathways.
STRING interaction network
for
Glycosaminoglycan metabolism
SuperPath